Akhenaten's cone-shaped head, elongated face, fingers and toes, pot belly and flaring hips have led some scholars to suggest that he had hydrocephalus or Marfan's syndrome. 阿肯纳坦的头圆锥形,脸、手指和脚趾较常人略长,大腹便便,臀部肥大,这使得某些学者认为他曾得过脑积水。
Background Progressive enlargement of the aortic root, leading to dissection, is the main cause of premature death in patients with Marfan's syndrome. 进行性扩张的主动脉根部导致的夹层是马凡综合症病人过早死亡的主要原因。
This mucin stain of the wall of the aorta demonstrates cystic medial necrosis, typical for Marfan's syndrome and causes the connective tissue weakness that explains the aortic dissection. 经过粘蛋白染色的主动脉壁可见囊状中层坏死,这不仅是马凡综合征的表现,度且从动脉切面可见结缔组织薄弱,导致主动脉剥离。
THE PERIOPERATIVE NURSING CARE OF 34 PATIENTS WITH LENS DISLOCATION SUBSEQUENT TO MARFAN'S SYNDROME Clinical analysis of cardiovascular complications and management on children Marfan syndrome 34例马方综合征晶状体脱位的围手术期护理儿童马方综合征的心血管并发症及其处理的临床分析
This aortic dissection occurred just above the aortic root in a patient with Marfan's syndrome. 马凡综合征病人见主动脉根部上部发生剥离,主动脉向上撕裂。
The exact cause is unknown, but risks include high blood pressure, smoking, atherosclerosis ( hardening of the arteries), trauma and Marfan's syndrome. 确切的发病机理未明,高危因素主要包括:高血压、吸烟、动脉粥样硬化、创伤及Marfan's综合症。
Clinical and Imaging Diagnosis of Marfan's Syndrome 马方综合征的临床影像诊断
Surgeries in16 cases ( 18 eyes) of children Marfan's syndrome are reviewed. 报告16例18眼儿童马方综合征晶状体半脱位的手术治疗。
Asymmetric pigmentary glaucoma in a patient with Marfan's syndrome 1例马方综合征患者眼部表现的不对称色素性青光眼
Vitrectomy Surgery for Lens Luxation of Marfan's Syndrome SURGICAL TREATMENT OF MARFAN SYNDROME 玻璃体切割术治疗Marfan氏综合征晶体脱位Marfan综合征的外科治疗
Objective To analyze the characteristics of cardiovascular two-dimensional ( 2-D) and Color Doppler echocardiography for patients with Marfan's syndrome. 目的分析马凡综合征心血管二维及彩色多普勒超声心动图特征,探讨其诊断价值。
Aortic root replacement on the beating heart to treat marfan's syndrome ( case report and review) 心脏跳动中主动脉根部替换术治疗马凡氏综合征(附1例报告及文献复习)
Beyond the root: Dilatation of the distal aorta in Marfan's syndrome 马方综合征患者远离主动脉根部的远端扩张
Methods 18 cases ( 29 eyes) of Marfan's syndrome complicated cataract with subluxated lens were implanted with capsular tension ring and posterior chamber intraocular lens ( IOL) after phacoemulsification. 方法18例(29眼)马凡综合征合并白内障晶状体半脱位接受超声乳化吸出术,将囊袋张力环植入晶状体囊袋后,再植入后房型人工晶状体。
Color Doppler echocardiography diagnosis of Marfan's syndrome 马凡综合征彩色多普勒超声心动图诊断
Surgical treatment of abdominal aortic aneurysm in marfan's syndrome Marfan综合征并发腹主动脉瘤的外科治疗
Method 23 cases of Marfan's syndrome were examined by transthoracic 2-D and Color Doppler echocardiography. 方法23例马凡综合征患者进行经胸壁二维及彩色多普勒超声心动图多切面检查。
Conclusion: Marfan's syndrome has characteristic CDE imaging, CDE is specific in the diagnosis of MS. 结论:MS心血管病变的CDE图像特征明显,CDE对MS心血管病变具有特异性诊断价值。
Results: Seventy-two cases ( 80%) with overt hypertension, 10 cases ( 11.1%) with Marfan's syndrome. 结果:72例(80%)有明确高血压,10例(11.1%)为马凡氏综合征。
Methods: From July to September of 1999,8 patients diagnosed as Marfan's syndrome with aortic root aneurysm and aortic incompetence underwent aortic root replacement using composite valve grafts. 方法:1999年7月至9月,对8例马凡综合征主动脉根部瘤合并主动脉瓣关闭不全患者以复合带瓣人工血管行主动脉根部置换术。
Medical Monitoring of Marfan's Syndrome in Athletes 运动员Marfan氏综合征的医务监督
Results: In the 21 cases of aortic aneurysms, there were 13 dissections and 2 Marfan's syndrome. 结果:21例中主动脉瘤6例,主动脉夹层13例,其中Ⅰ型4例,Ⅱ型1例,Ⅲ型8例,马凡氏综合征2例。
Objective To observe the operative outcomes of Marfan's syndrome. 目的观察马凡氏综合征心血管病变手术治疗效果。
Objective To study the significance of microsatellite detection for presymptomatic diagnosis of Marfan's syndrome. 目的探讨FBN1基因微卫星检测对Marfan综合征(MFS)症状前诊断的应用价值。
Objective: To establish a haplotype segregation method using the microsatellite polymorphism in families with Marfan's syndrome ( MFS) for early diagnosis, management, and genetic counseling. To evaluate microsatellite detection in presymptomatic diagnosis of Marfan's syndrome. 目的建立一种微卫星多态性检测法对MFS家系成员进行原纤蛋白-1基因(FBN1)单倍型分离分析,探讨FBN微卫星检测对Marfan综合征(MFS)症状前诊断的应用价值。
Methods A retrospective analysis was made on cardiovascular features of 28 cases of Marfan's syndrome, and a comparison with a control group of 20 normal cases was also made. 方法回顾性分析28例马凡综合征心脏大血管的MRI表现,并与20例正常组进行对照分析。
We report here three new DNA sequences of Fibrillin 1 ( FBN1), and analyse their significance in diagnoses of untypical Marfan's syndrome. 报道3种新的FBN1片段的DNA序列,并分析这些新序列在1例非典型性马凡综合症基因诊断中的参考意义。
Methods Collecting 32 cases of Marfan's syndrome operated in our hospital and analyzing the changes of cardiac function between preoperation and 6~ 12 months postoperation. 方法收集在我院手术治疗的马凡氏综合征患者32例,对比分析他们手术前及手术后6~12个月心功能变化情况。
An Imaging Study on Ascending Aortic Lesions of 17 Cases of Marfan's Syndrome 马凡综合征升主动脉病变17例影像分析
Surgical Treatment for 32 Cases of Marfan's Syndrome 马凡氏综合征32例外科治疗